概述
What is Idiopathic Pulmonary Fibrosis
Idiopathic pulmonary fibrosis (IPF) is a chronic, progressive lung disease characterized by progressive lung scarring and the histological picture of usual interstitial pneumonia (UIP). IPF is the most common and most lethal type of interstitial lung disease (ILD).
How common is Idiopathic Pulmonary Fibrosis
The estimated prevalence of IPF in the United States varies between 14 and 27.9 cases per 100,000 of the population, while incidence of IPF in the U.S. is estimated at 6.8 to 8.8 cases per 100,000.1 IPF is diagnosed more commonly in men vs. women and most commonly diagnosed in patients age 75 or older. Idiopathic Pulmonary Fibrosis newly occurs in approximately 12 per 100,000 people per year.
Questions regarding your Idiopathic Pulmonary Fibrosis therapy
您可以随时通过电话或网络与 Accredo 肺动脉高压护理团队取得联系，该团队全天不间断服务。
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- 1Luba Nalysnyk, Javier Cid-Ruzafa, Philip Rotella, Dirk Esser. European Respiratory Review Dec 2012, 21 (126) 355-361; DOI: 10.1183/09059180.00002512
症状
What are the symptoms of Idiopathic Pulmonary Fibrosis
Symptoms of IPF may include:
- Exertional dyspnea
- Labored breathing
- 干咳
- Muscle and joint aches
- 乏力（也称为疲劳）
- 食欲不振
- 体重减轻
- Clubbing (rounding of the tips of the fingers or toes)
如何诊断
The diagnosis of idiopathic pulmonary fibrosis can be challenging. Signs and symptoms can be very similar to other interstitial lung disease disorders. Additionally, other disease states can display signs and symptoms similar to IPF, therefore ruling out other disorders is essential before making a diagnosis.
验血
Blood tests can detect oxygen or carbon dioxide level abnormalities that could assist in the diagnosis of IPF.
影像检查
A chest radiograph (X-ray) can be used to assist in the diagnosis, although it is not diagnostic on its own. Chest radiographs are low sensitivity and would show lower lobe volume loss in more advanced disease states. A High-resolution computed tomography (HRCT) is the gold standard for IPF diagnosis. It has excellent specificity and can diagnosis IPF through the presence of “honeycombing” patterns in the lungs.
肺功能检查
这些检查会测量肺部可以容纳的空气量、进出肺部的空气量以及肺部交换氧气的能力。执行这些检查可能会确定其原因。Specific pulmonary function tests include Spirometry and diffusion capacity and Oximetry.
Lung tissue analysis
Tissue samples of a patient’s lung can be helpful in determining diagnosis of idiopathic pulmonary fibrosis. Bronchoscopy, bronchoalveolar lavage, and surgical biopsy are particular ways in which tissue samples can be collected.
High resolution computerized tomography
This imaging test is key to, and sometimes the first step in, the diagnosis of idiopathic pulmonary fibrosis. CT scanners use a computer to combine X-ray images taken from many different angles to produce cross-sectional images of internal structures. A high-resolution CT scan can be particularly helpful in determining the extent of lung damage caused by IPF. It can show details of the fibrosis, which can be helpful in narrowing down the diagnosis of IPF, which is characterized as a “honeycombing” pattern.
药品
Idiopathic Pulmonary Fibrosis (IPF) Medications
While there is currently no cure for IPF, different treatment options are available to help you manage your disease and feel better day-to-day. Your doctor may prescribe other medication(s) as part of your treatment based on your particular symptoms and level of severity. The following specialty medication is available at Accredo for the treatment of IPF.
节约护理费用
您还可获得经济援助协调服务，以承担您的部分药品费用，包括生产商和社区计划。Accredo 代表可以帮助您找到适合您的计划。
社区财政资源
- PSI-Patient Services, Inc. | 800-366-7741
- 患者权益基金会 | 800-532-5274
- 援助基金 | 855-845-3663
- Healthwell 基金会 | 800- 675-8416
- Esbriet® (pirfenidone) Financial Assistance & Copay Information | 844-693-7274
- Ofev® (nintedanib) Capsules Financial Assistance Information | 855-297-5906
财政指导
急救性质的特殊药品很昂贵。通过此视频，了解 Accredo 团队如何帮助个人找到可以负担他们救命药品费用的方式。
查找支持
There are organizations that support research and advocacy for pulmonary fibrosis. 下面是其中部分组织。
支持组织
政府组织
团队介绍
Accredo’s Idiopathic pulmonary fibrosis care team is dedicated to serving you and we understand the complexity of your condition. 我们的特殊培训临床医师每周 7 天、每天 24 小时为您提供服务，以回答您的任何问题。
我们为什么要这样做
Accredo 为慢性和复杂病症患者提供支持，并帮助他们过上最好的生活。请观看我们的视频，了解我们为什么为患者尽心尽力。